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. Author manuscript; available in PMC: 2014 Apr 1.
Published in final edited form as: Autoimmun Rev. 2012 Nov 29;12(6):687–689. doi: 10.1016/j.autrev.2012.10.017

Table 1.

Non-infectious complications of CVID

Category Condition Percentage*
Pulmonary Chronic lung disease 28%
Bronchiectasis 11%
Gastrointestinal Inflammatory bowel disease 20%
Malabsorption 6%
Chronic diarrhea 2%
Autoimmune Idiopathic thrombocytopenic purpura 14%
Autoimmune hemolytic anemia 7%
Evan’s syndrome 4%
Rheumatoid arthritis 3%
Others: neutropenia, pernicious anemia, diabetes mellitus, multiple sclerosis, juvenile idiopathic arthritis, autoimmune thyroiditis, vasculitis, systemic lupus erythematosus <1%
Granulomatous disease Lung, liver, lymph nodes, skin 10%
Malignancy Lymphoid malignancy 8%
Breast cancer 2%
Gastric carcinoma <1%
*

From ResnickE. et al. Blood (2012) 119: 1650–1657