Table 2.
Sequence variants in PLA2R1 observed in 60 anti-PLA2R1–positive patients
Chr | Position | Name | Ref | All | CEU AF | AF Patients | P Value | Ref cDNA | cDNA | Prot Level | Effect | Exon | Observations |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|
2 | 160808075 | rs3828323a | C | C/T | 0.511 | 0.381 | 0.0090 | G | c.3316G>A | p.Gly1106Ser | Missense | 24 | Linker region between CTLD6 and CTLD7 |
2 | 160808076 | rs72954858 | G | G/A | 0.012 | 0.042 | 0.014 | C | c.3315C>T | p.His1105= | Synonymous | 24 | Linker region between CTLD6 and CTLD7 |
2 | 160833188 | rs2715918a | A | A/G | 0.821 | 0.700 | 0.0020 | T | c.2437+8T>C | Intron | 16 | ||
2b | 160840584 | rs149133741 | C | A/C | 0.005 | 0.008 | G | c.2038G>T | p.Val680Leu | Missense | 13 | CTLD4 | |
2b | 160862197 | rs149960520 | C | C/T | 0c | 0.008 | G | c.1800G>A | p.Pro600= | Synonymous | 11 | CTLD3 | |
2b | 160873180 | rs140427239 | T | C/T | 0 | 0.008 | A | c.1496A>G | p.Tyr499Cys | Missense | 9 | CTLD2 2 aa from C4 | |
2 | 160879259 | rs33985939 | C | C/T | 0.094 | 0.038 | 0.055 | G | c.1211G>A | p.Arg404His | Missense | 7 | CTLD2 1 aa from C1 |
2 | 160885418 | rs35771982a | G | G/C | 0.480 | 0.250 | 0.0000035 | C | c.898C>G | p.His300Asp | Missense | 5 | CTLD1 |
2 | 160885442 | rs3749117a | T | T/C | 0.485 | 0.250 | 0.0000021 | A | c.874A>G | p.Met292Val | Missense | 5 | WMGL motif of CTLD1 |
2b | 160889495 | rs149256089 | A | A/G | 0.001c | 0.008 | T | c.816T>C | p.Asp272= | Synonymous | 4 | CTLD1 | |
2 | 160901517 | rs4665143a | A | A/G | 0.629 | 0.430 | 0.000049 | T | c.261T>C | p.Ser87= | Synonymous | 2 | CRD |
2 | 160918984 | rs925409 | T | T/A | 0.074 | 0.068 | 0.81 | A | c.-70A>T | 5′-UTR | 1 | ||
2 | 160919020 | rs3749119a | C | C/T | 0.339 | 0.152 | 0.000049 | G | c.-106G>A | 5′-UTR | 1 |
Chr, chromosome; position, base pair position based on University of California, Santa Cruz, genome browser version human (February 2009) (GRCh37/hg19) assembly NC_000002.11; name, rs identifier; ref, genomic reference allele; all, alleles; CEU AF, variation allele frequencies white population from 1000 Genomes release 10 (March 2012); AF patients, patient variation allele frequencies; P value, comparison of variation allele frequencies in controls and patients; ref cDNA, reference allele cDNA (given that PLA2R1 is on the negative strand); cDNA, NM_007366.4; prot level, NP_031392.3; aa, amino acid; WMGL, motif; FNII, fibronectin type II domain; CRD, cysteine-rich domain; UTR, untranslated region.
Significantly associated with iMN.
Rare variants.
Not reported in 1000 Genomes; allele frequency from Single Nucleotide Polymorphism Database, release 136.