Table III.

Haematological parameters of DBA patients with elevated vs. normal eADA^*

Parameter	eADA ≥ 1 iu/g of Hb	eADA <1 iu/g of Hb	P
Hb (g/l)
No. of patients	27	6
median (range)	123 (69–155)	118 (85–140)	0.44
No. of patients anaemic (%)†	10 (37)	3 (50)	0.66
Correlation coefficient			0.31
MCV (fl)
No. of patients	27	6
median (range)	97 (70–123)	97 (89–106)	0.95
No. of patients macrocytic (%)†	13 (48)	3 (50)	1
Correlation coefficient			0.32
Epo (mu/ml)
No. of patients	16	4
median (range)	28 (8.6–559)	33 (10–124)	0.56
No. of patients with Epo >25 (%)†	9 (56)	2 (66)	1
Correlation coefficient			0.5
Hb F
No. of patients	24	4
median (range) %	1.5 (0–12.5)	0.9 (0–4.1)	0.4
median (range) g/l	2.0 (0–10)	1.0 (0–5.0)	0.4
No. of patients with Hb F >1 % (%)†	12 (50)	1 (25)	0.6
Correlation coefficient			0.34

DBA, Diamond-Blackfan anaemia; eADA, erythrocyte adenosine deaminase; Hb, haemoglobin; MCV, mean corpuscular volume; Epo, erythropoietin; Hb F, fetal haemoglobin.

^*Not every patient in the cohort had concurrent blood test results for haematological parameters.

^†Based on standards for age (Brugnara et al, 2009).