Table 2.
Descriptive characteristics of the study population during baseline visit and after 6 months divided into CNAQ scores (CNAQ ≤ 28 and CNAQ >28). Numbers show mean, SD, and range.
| Characteristics | CNAQ≤28 n (%) or mean (SD, range) |
CNAQ>28 n (%) or mean (SD, range) |
| Female: Male | 7:17 | 10:17 |
| Age at onset, mean (SD, range) | 57.8 (10,0, 36-72) | 54.4 (8.1, 37-69) |
| Duration of disease (months), mean (SD, range) | 27.7 (23.8, 3-125) | 35.1 (25.8, 4-104) |
| ALSFRS-R score at baseline, mean (SD, range) | 33.1 (8.0, 16-47) | 33 (8., 16-44) |
| ALSFRS-R score after 6 months, mean (SD, range) | 25.9 (8.5, 15-40) | 30.6 (9.0, 17-44) |
| BMI (kg/m2) at baseline, mean (SD, range) | 23.1 (3.5, 19-32) | 24.1 (3.4, 17-32) |
| BMI (kg/m2) after 6 months, mean (SD, range) | 21.6 (3.3, 17-29) | 23.2 (3.7, 18-30) |
| Vital Capacity at baseline, % mean (SD, range) | 64.8 (23.2, 24-103) | 70.7 (26.4, 23-107) |
| Spinal onset, n (%) | 20 (83) | 16 (59) |
| Bulbar onset, n (%) | 3 (13) | 10 (37) |
| Axial onset, n (%) | 1 (4) | 1 (4) |
| NIV, n (%) | 4 (17) | 8 (30) |
| Deceased, n (%) | 7 (29) | 2 (7) |