Table 3.

Clinical manifestations, medications and intervention characteristics in the registrants with DMD and BMD

	DMD patients		BMD patients
	No. of case	% of cases	No. of case	% of cases
Walking capability
Normal walking	254	43.6%	80	76.2%
Not able to walk, and sit without support	184	31.6%	19	18.1%
Not able to sit without support	145	24.9%	6	5.7%
	583	100.0%	105	100.0%
Cardiac function
Normal	392	67.2%	76	72.4%
Dysfunction	180	30.9%	28	26.7%
Not performed	11	1.9%	1	1.0%
	583	100.0%	105	100.0%
Respiratory function
Normal	65	11.1%	45	42.9%
Dysfunction	202	34.6%	18	17.1%
Not performed	316	54.2%	42	40.0%
	583	100.0%	105	100.0%
Steroid use
Current	171	29.3%	6	5.7%
Used to	69	11.8%	6	5.7%
Never	343	58.8%	93	88.6%
	583	100.0%	105	100.0%
Cardiac medication
Prescribed	172	29.5%	25	23.8%
Not prescribed	411	70.5%	80	76.2%
	583	100.0%	105	100.0%
Drug
β-blocker	94	54.7%	16	64.0%
ACE-inhibitor	140	81.4%	19	76.0%
ARB	12	7.0%	5	20.0%
Diuretics	43	25.0%	7	28.0%
Other	29	16.9%	7	28.0%
	172*1	100%	25*1	100%
Mechanical ventilation
No	455	78.0%	103	98.1%
Yes	128	22.0%	2	1.9%
	583	100.0%	105	100.0%
Invasive	20	15.6%	2	100.0%
Non-invasive	108	84.4%	0	0.0%
	128*2	100.0%	2*2	100.0%
Temporal	71	55.5%	0	0.0%
Continuous	57	44.5%	2	100.0%
	128*2	100.0%	2*2	100.0%
Scoliosis surgery
Yes	23	3.9%	1	1.0%
No	560	96.1%	103	98.1%
Not described	0	0.0%	1	1.0%
	583	100.0%	105	100.0%

*1; The number of registrants who were prescribed with cardiovascular medicines.

*2; The number of registrants using ventilator support.