Table 3.
|
DMD patients |
BMD patients |
||
---|---|---|---|---|
No. of case | % of cases | No. of case | % of cases | |
Walking capability |
|
|
|
|
Normal walking |
254 |
43.6% |
80 |
76.2% |
Not able to walk, and sit without support |
184 |
31.6% |
19 |
18.1% |
Not able to sit without support |
145 |
24.9% |
6 |
5.7% |
|
583 |
100.0% |
105 |
100.0% |
Cardiac function |
|
|
|
|
Normal |
392 |
67.2% |
76 |
72.4% |
Dysfunction |
180 |
30.9% |
28 |
26.7% |
Not performed |
11 |
1.9% |
1 |
1.0% |
|
583 |
100.0% |
105 |
100.0% |
Respiratory function |
|
|
|
|
Normal |
65 |
11.1% |
45 |
42.9% |
Dysfunction |
202 |
34.6% |
18 |
17.1% |
Not performed |
316 |
54.2% |
42 |
40.0% |
|
583 |
100.0% |
105 |
100.0% |
Steroid use |
|
|
|
|
Current |
171 |
29.3% |
6 |
5.7% |
Used to |
69 |
11.8% |
6 |
5.7% |
Never |
343 |
58.8% |
93 |
88.6% |
|
583 |
100.0% |
105 |
100.0% |
Cardiac medication |
|
|
|
|
Prescribed |
172 |
29.5% |
25 |
23.8% |
Not prescribed |
411 |
70.5% |
80 |
76.2% |
|
583 |
100.0% |
105 |
100.0% |
Drug |
|
|
|
|
β-blocker |
94 |
54.7% |
16 |
64.0% |
ACE-inhibitor |
140 |
81.4% |
19 |
76.0% |
ARB |
12 |
7.0% |
5 |
20.0% |
Diuretics |
43 |
25.0% |
7 |
28.0% |
Other |
29 |
16.9% |
7 |
28.0% |
|
172*1 |
100% |
25*1 |
100% |
Mechanical ventilation |
|
|
|
|
No |
455 |
78.0% |
103 |
98.1% |
Yes |
128 |
22.0% |
2 |
1.9% |
|
583 |
100.0% |
105 |
100.0% |
Invasive |
20 |
15.6% |
2 |
100.0% |
Non-invasive |
108 |
84.4% |
0 |
0.0% |
|
128*2 |
100.0% |
2*2 |
100.0% |
Temporal |
71 |
55.5% |
0 |
0.0% |
Continuous |
57 |
44.5% |
2 |
100.0% |
|
128*2 |
100.0% |
2*2 |
100.0% |
Scoliosis surgery |
|
|
|
|
Yes |
23 |
3.9% |
1 |
1.0% |
No |
560 |
96.1% |
103 |
98.1% |
Not described |
0 |
0.0% |
1 |
1.0% |
583 | 100.0% | 105 | 100.0% |
*1; The number of registrants who were prescribed with cardiovascular medicines.
*2; The number of registrants using ventilator support.