Table 1. Demographic and clinical characteristics of the 102 patients with chronic periaortitis* &.
Mean age at disease onset ± SD (years) | 58±12 |
Males/females | 65.7/34.3 |
Idiopathic retroperitoneal fibrosis | 83/102 (81.4) |
Inflammatory abdominal aortic aneurysms | 19/102 (18.6) |
Retroperitoneal fibrosis localisation | |
Periaortic-iliac | 41/102 (40.2) |
Periaortic-iliac+pericaval | 53/102 (52.0) |
Atypical localisation | 8/102 (7.8) |
Thoracic vessel or mediastinal involvement | 22/58 (37.9) |
Presence of atherosclerotic disease (at diagnosis or during follow-up)** | 26/101 (25.7) |
Systemic symptoms and/or signs§ | 76/100 (76.0) |
Abdominal/lumbar pain | 85/101 (84.2) |
Constipation | 29/99 (29.3) |
Testicular symptoms | 39/65 (60.0) |
Deep vein thrombosis | 16/100 (16.0) |
Ureteral obstruction | 77/102 (75.5) |
Unilateral | 28/102 (27.5) |
Bilateral | 50/102 (49.0) |
Acute renal failure | 49/102 (48.0) |
Conservative treatment (stents, nephrostomies) | 41/102 (40.2) |
Surgical ureterolysis | 28/102 (27.5) |
Retroperitoneal biopsy | 55/101 (54.5) |
Associated autoimmune/inflammatory diseases | 41/95 (43.2) |
Autoimmune thyroiditis | 20/88 (22.7) |
ANA positivity | 32/97 (33.0) |
Other positive autoantibodies | 46/96 (47.9) |
Mean duration of follow-up ± SD (months) | 42.5±38.7 |
Mean ESR at diagnosis ± SD (mm/hour) | 68±32 |
Mean CRP level at diagnosis ± SD (mg/L) | 41.4±43.6 |
Values indicate the percentage of patients unless otherwise indicated.
Some characteristics were not available for all 102 patients.
Atherosclerotic disease: the presence of coronary artery disease, cerebrovascular disease or peripheral arterial disease.
Fever, anorexia, and weight loss.
ANA = antinuclear antibodies; ESR = erythrocyte sedimentation rate; CRP = C-reactive protein.