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. Author manuscript; available in PMC: 2013 May 21.
Published in final edited form as: J Neuropathol Exp Neurol. 2008 Jun;67(6):555–564. doi: 10.1097/NEN.0b013e31817713b5

TABLE 3.

Presence and Distribution of TDP-43 Pathology in CBD

CBD (n = 39)

TDP-43 Negative TDP-43 Positive
No. cases 33 6
Percentage 84.6 15.4
Male/female 14/19 3/3
Mean age at death (SD), years 67.8 (6.8) 66.0 (10.5)
Mean disease duration (SD), years 4.4 (2.1) 5.2 (1.7)
TDP-43 pathology
  Dentate granule cells 0 6
  Entorhinal cortex 0 6
  Temporal cortex 0 4
  Frontal cortex 0 4
  NIIs 0 3

CBD, corticobasal degeneration; NII, neuronal intranuclear inclusion; SD, standard deviation; TDP-43, TAR-DNA/binding protein 43.