Table 1. Comparison of clinical and electrocardiographic findings in myotonic dystrophy type 1 patients with normal and abnormal echocardiogram.
Parameter | Total (n=27) | Normal ECHO (n=17) | Abnormal ECHO (n=10) |
---|---|---|---|
Age (years) | 39.1±14.1 | 47.4±11.10 | 34.2±13.6* |
Male | 16 | 9 | 7 |
Female | 11 | 8 | 3 |
Duration of illness (years) | 21.0±13.3 | 17.4±2.8 | 25.9±13.2 |
Cardiac symptoms | 8 | 5 | 3 |
PR interval >200 ms | 8 | 2 | 6 |
Left anterior fascicular block | 7 | 5 | 2 |
QTc ms | 414.6±30.1 | 414.0±27.8 | 415.5±34.7 |
Proximal weakness | 19 | 11 | 8 |
Severe distal weakness (MRC <4) | 13 | 7 | 6 |
Congenital myotonic dystrophy | 6 | 5 | 1 |
P=0.017