Table 2. Characteristics of adult myotonic dystrophy type 1 patients with systolic dysfunction.
| N. | LVEF (%) | Age (years) | Duration illness (years) | Other ECHO abnormality | EKG | Weakness proximal/distal <4 |
|---|---|---|---|---|---|---|
| 1 | 50 | 40 | 11 | None | Normal | Y/Y |
| 16 | 37 | 34 | 9 | None | A Fib | N/N |
| 19 | 50 | 27 | 27* | Apical hypokinesia | LAFB | Y/N |
| 23 | 35 | 52 | 27 | None | AVB1 | Y/Y |
| 28 | 40 | 47 | 6 | Left atrial dilatation | AFL AVB1 | Y/Y |
*
Congenital myotonic dystrophy. LVEF, left ventricular ejection fraction; ECHO, echocardiogram; EKG, electrocardiogram; AVB1, first degree atrioventricular block; LAFB, left anterior fascicular block; AFL, atrial flutter; A Fib, atrial fibrillation.