Table 1.
No. | Authors (yr.) | Diagnosis | Age (year)/Gender | Tumor size (cm) | Nuclear grade | Cellularity | MF (per 50HPF) | Invasion | Necrosis | LN status | Treatment | Outcome |
---|---|---|---|---|---|---|---|---|---|---|---|---|
1 |
Folpe AL (2005) [3] |
PEComa with UMP |
67/Female |
13.0 |
High |
Moderate |
0 |
No |
No |
Not involved |
SE only |
NED at 84 months |
2 |
|
Benign PEComa |
97/Female |
4.0 |
Intermediate |
Moderate |
0 |
No |
No |
Not involved |
SE only |
NED at 38 months |
3 |
|
Malignant PEComa |
80/Female |
9.5 |
High |
High |
>50 |
Vascular invasion |
Yes |
Not involved |
SE only |
NED at 19 months |
4 |
|
Malignant PEComa |
46/Female |
12.0 |
Intermediate |
Moderate |
5 |
Vascular invasion |
Yes |
Not involved |
SE + CT |
Recur and liver metastases at 22 months; die at 27 months |
5 |
Gross E (2010) [4] |
Malignant PEComa |
5.5/Male |
5.0 |
High |
Moderate |
NA |
Surrounding tissue invasion |
No |
Not involved |
SE only |
NED at 24 months |
6 |
Lai CL (2012) [5] |
Malignant PEComa |
59/Male |
11.0 |
High |
High |
3 |
Vascular invasion |
Yes |
Not involved |
SE + CT |
Recur at 6 months; alive |
7 | The present case | Malignant PEComa | 38/Female | 10.0 | Intermediate | Moderate | 2 | Surrounding tissue invasion | Yes | Involved | SE + CT | NED at 6 months |
UMP, uncertain malignant potential; MF, mitotic figure; LN, lymph node; SE, surgical excision; CT, chemotherapy; NA, not available; NED, no evidence of disease.