Table 1. Classification of anti-neuronal antibodies.
| Antigen | Associated syndromes | How to test | Commercially available |
|---|---|---|---|
| Group I | |||
| Hu (ANNA1) | Encephalomyelitis, PCD, LE, brainstem encephalitis, sensory neuropathy | TBA, IB | yes |
| CV2 (CRMP5) | Encephalomyelitis, Chorea, PCD, LE, sensomotoric neuropathy | TBA, IB | yes |
| Amphiphysin | SPS, myelopathy and myoclonus, Encephalomyelitis | TBA, IB | yes |
| Yo (PCA1) | PCD | TBA, IB | yes |
| Ri (ANNA2) | Brainstem encephalitis, Opsoclonus myoclonus | TBA, IB | yes |
| MA-2 | LE, brainstem encephalitis | TBA, IB | yes |
| SOX1 (AGNA) | Encephalomyelitis, PCD | TBA, IB | yes |
| GAD65 | SPS, cerebellar ataxia, LE | TBA, IB | yes |
| Tr (DNER) | PCD | TBA, CBA | no |
| Group II | |||
| NMDAR | encephalitis | TBA, CBA | yes |
| LGI1 | LE | TBA, CBA | yes |
| GABABR | LE | TBA, CBA | yes |
| AMPAR | LE | TBA, CBA | yes |
| CASPR2 | Morvan’s syndrome | TBA, CBA | yes |
| GlyR | PERM | CBA | no |
| mGluR1 | Cerebellar ataxia | TBA, CBA | no |
| mGluR5 | LE | TBA, CBA | no |
| VGCC | LEMS, PCD | RIA | yes |
| Aquaporin-4 (glial) | NMO | TBA, CBA | yes |