Table 1.

Summary of clinical features of 22 patients

Age (years)			CT			PTA		Vertigo	Thyroid
			EVA	MD	VE	HL (dB)	Conductive hearing loss		Goiter	Thyroid function
1	3	R	+	+	+	SO	unknown	-	-	normal
		L	+	+	+	SO	unknown
2	14	R	+	+	-	105	+	-	+	normal
		L	+	+	-	96	+
3	21	R	+	+	+	73	+	+	+	normal
		L	+	+	+	91	+
4	21	R	+	-	-	81	+	+	+	normal
		L	+	-	-	85	+
5	28	R	+	+	+	96	+	+	+	normal
		L	+	+	+	SO	+
6	33	R	+	+	-	101	+	+	+	normal
		L	+	+	+	106	+
7	1	R	+	+	-	SO	unknown	-	-	normal
		L	+	+	+	SO	unknown
8	1	R	+	-	-	SO	unknown	-	-	normal
		L	+	-	-	103	unknown
9	2	R	+	+	-	101	unknown	-	-	normal
		L	+	+	-	100	unknown
10	12	R	+	-	-	95	+	-	+	normal
		L	+	-	-	100	+
11	29	R	+	+	+	85	+	-	-
		L	+	+	+	110	+
12	0	R	+	-	-	55	unknown	+	-	normal
		L	+	-	-	73	unknown
13	3	R	+	-	+	85	unknown	+	-	normal
		L	+	+	+	58	+
14	5	R	+	+	+	95	+	+	-	normal
		L	+	+	+	93	+
15	5	R	+	+	+	103	+	-	-	normal
		L	+	+	+	100	unknown
16	6	R	+	-	-	81	+	+	-	normal
		L	+	-	-	91	+
17	7	R	+	-	-	83	+	-	-	normal
		L	+	-	+	81	+
18	14	R	+	+	+	96	+	-	+	normal
		L	+	+	+	91	+
19	16	R	+	-	+	91	+	-	+	normal
		L	-	-	+	21	-
20	26	R	+	-	-	98	+	+	-	normal
		L	+	-	+	103	+
21	5	R	+	+	+	85	+	-	-	normal
		L	+	+	-	97	+
22	10	R	+	-	-	53	+	-	-	normal
		L	-	-	-	15	-

EVA enlarged vestibular aqueduct, MD Mondini malformation, VE vestibular enlargement, PTA pure tone audiogram, HL hearing level, SO scale out, NA no available data.