Table 1.
ILAR classification of JIA, in agreement with the ILAR conference of 2001 in Edmonton1
| No. | Subtypes of JIA | Extra-articular manifestations | Disqualifying criteria |
| 1 | Systemic arthritis (Still's syndrome) | Fever, exanthema, pleuritis, hepatosplenomegaly, pericarditis, dystrophia, lymphadenopathia, vasculitis, short stature | a,b,c,d |
| ICD-10: M08.2 | |||
| 2 | Seronegative polyarthritis (RF−) | Subfebrile temperatures, tenosynovitis, uveitis, vasculitis | a,b,c,d,e |
| ICD-10: M08.3 | |||
| 3 | Seropositive polyarthritis (RF+) | Subfebrile temperatures, tenosynovitis, rheumatic nodes | a,b,c,d |
| ICD-10: M08.0 | |||
| 4 | Oligoarthritis | Chronic uveitis | a,b,c,d,e |
| ICD-10: M08.4 | |||
| 5 | Psoriatic arthritis | Psoriasis | b,c |
| ICD-10: L40.5/M09. | |||
| 6 | Enthesitis-associated arthritis | Arthritis and enthesitis, acute uveitis, sacroiliitis, Reiter syndrome, ankylosing spondylitis | a,d,e |
| ICD-10: M08.1 | |||
| 7 | Undifferentiated arthritis | ||
| ICD-10: M08.8 |
ICD, (World Health Organization) International Classification of Diseases; ILAR, International League of Associations for Rheumatology; JIA, juvenile idiopathic arthritis.
Disqualifying criteria: a, psoriasis in patients or psoriasis of relatives in first degree; b, human leukocyte antigen B27 positive form, male gender or older than 6 years; c, ankylosing spondylitis, enthesitis associated arthritis, sacroiliitis with chronic and inflammatory intestinal diseases, Reiter syndrome in patients or relatives in first degree; d, rheuma factor repeatedly provable within an interval of at least 3 months; e, systemic signs of disease.
Source: Petty RE, Southwood TR, Manners P, Baum J, Glass DN, Goldenberg J. International League of Associations for Rheumatology classification of juvenile idiopathic arthritis: second revision, Edmonton, 2001. J Rheumatol 2004; 31: 390–392.