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. 2013 Jun 13;86(2):255–260.

Table 1. Characteristics of refractory MG patients.

Patient Antibody status Gender/Age of onset Refractory Criteriaa Previous MG therapiesb
1 MuSK F/53 1, 2, 3 Az, PPX
2 MuSK F/51 1, 2, 3 Az, IVIG, Pyr
3 MuSK F/29 1, 2, 3 IVIG, PPX, Thy
4 MuSK F/28 1, 3 Pyr, Thy
5 MuSK F/36 1, 2, 3 IVIG, Pyr
6 MuSK F/17 1, 2, 3 Az, IVIG, Pyr, Thy
7 MuSK F/20 1, 2, 3 P, PPX
8 MuSK F/43 1, 2, 3 Cs, IVIG, MM, MTX, Pyr, PPX, Ta, Thy
9 MuSK M/62 1, 2, 3 IVIG, MM, P
10 AChR M/24 2 P, PPX, Pyr, Thy
11 AChR M/59 1, 2, 3 Az, IVIG, P
12 AChR M/62 1, 2, 3 Az, IVIG, P, PPX, Thy
13 AChR M/28 1 Az, MM, P, Pyr, PPX, Thy
14 AChR F/17 2, 3 IVIG, P, PPX, Pyr, Thy
15 AChR F/35 1, 2, 3 Az, P, PPX, Thy
16 AChR F/48 1, 2, 3 Az, IVIG, P, PPX, Pyr, Thy
17 AChR F/50 1, 2, 3 Az, MM, P, PPX, Pyr, Thy
18 AChR F/35 2 IVIG, P, Pyr, Thy
19 AChR F/35 1, 3 Az, P, Thy

aRefractory Criteria: (1) inability to lower immunotherapy without clinical relapse, (2) not clinically controlled on immunotherapy regimen, (3) severe side effects from immunotherapy.

bAz, azathioprine; Cs, cyclosporine; IVIG, intravenous immunoglobulin; MM, mycophenolate mofetil; MTX, methotrexate; P, prednisone; PPX, plasma exchange; Pyr, pyridostigmine; Ta, tacrolimus; Thy, thymectomy.