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. Author manuscript; available in PMC: 2013 Sep 1.
Published in final edited form as: J Child Neurol. 2012 Jun 29;27(9):1133–1137. doi: 10.1177/0883073812448230

Table 3.

Major Clinical Features of FRDA and Their Frequency from 3 Studies47

Symptom Harding14 Durr8 Delatycki7
Ataxia 99 100 100
Dysarthria 97 91 95
Absent lower limb reflexes 99 87 74
Scoliosis 79 60 78
Pes cavus 55 55 74
Swallowing disturbance - 27 -
Sphincter disturbance - 23 41
Reduced vision 18 13 -
Hearing impairment 8 13 -
Cardiomyopathy on echocardiogram - 63 65
Diabetes/abnormal glucose tolerance 10 32 8