Table 1.

Peak FVC and Genetic Data

Sibship Number	Patient	Exons Involved	Age at Peak FVC (y)	Peak FVC Level (L)
Discordant Sibships
1	1	51	13.42	1.97
	2		14.17	2.88
	3		14.5	2.71
2	1	44	17	3.62
	2		11.33	2.67
3	1	31	18.33	3.38
	2		18.17	4.6
Concordant Sibships
4	1	45–50	14.67	2.48
	2		15.08	2.81
5	1	52	11.08	1.5
	2		13.08	2.04
6	1	44	12.42	1.4
	2		12.83	1.44
7	1	56	14	2.02
	2		14.5	1.67

Mean age at peak FVC +/− S.D. = 14.31 +/− 2.18 years

Abbreviation: FVC, forced vital capacity.