Table 2.

Clinical Characteristics of PFAPA Patients with Variants in the MEFV Gene Compared with those of PFAPA Patients without MEFV Variants

	Patients with MEFV Variants (n=13)	Patients without MEFV Variants (n=7)	P Value
Age at onset (years)	2.8±1.9	3.2±1.9	NS
Age at Diagnosis (years)	4.3±2.2	4.9±1.9	NS
Male: female ratio	5/8	4/3	NS
Family history of PFAPA	4/9	3/4	NS
Attack duration (days)	3.6±0.86	5.3±1.89	P=0.0174
Interval between attacks (weeks)	4.9±1.59	5.5±0.96	NS
Cyclic periodic attacks	5/13	4/7	NS
Pharyngitis	13/13	7/7	NS
Aphthae	7/13	5/7	NS
Enlarged tonsillitis	13/13	7/7	NS
Abdominal pains	1/13	2/7	NS
Musculoskeletal Pains	1/13	2/7	NS
Headaches	4/13	5/7	NS
WBC/μL	143±41	142±41	NS
ESR mm/h	87±23	72±14	NS
CRP levels mg/dL	6.52±3.53	5.87±2.85	NS

NS: not significant.