Table 1.

Names and definitions of vasculitis adopted by the Chapel Hill Consensus Conference (NC, USA) on the nomenclature of systemic vasculitis.

Diagnosis	Description
Granulomatosis with polyangiitis	Granulomatous inflammation involving the respiratory tract and necrotizing vasculitis affecting small-to-medium sized vessels (e.g., capillaries, venules, arterioles and arteries. Necrotizing glomerulonephritis is common
Giant cell arteritis	Granulomatous arteritis of the aorta and its major branches, with a predilection for the extracranial branches of the carotid artery. Often involves the temporal artery. Usually occurs in patients older than 50 years of age and is often associated with polymyalgia rheumatica
Takayasu’s arteritis	Granulomatous inflammation of the aorta and its major branches. Usually occurs in patients younger than 50 years of age
Microscopic polyangiitis	Necrotizing vasculitis, with few or no immune deposits, affecting small vessels (i.e., capillaries, venules or arterioles). Necrotizing arteritis involving small- and medium-sized arteries may be present Necrotizing glomerulonephritis is very common. Pulmonary capillaritis often occurs
Essential cryoglobulinemic vasculitis	Vasculitis, with cryoglobulin immune deposits, affecting small vessels (i.e., capillaries, venules or arterioles), and is associated with cryoglobulins in serum. Skin and glomeruli are often involved

Data taken from [57].