Skip to main content
. Author manuscript; available in PMC: 2013 Jun 17.
Published in final edited form as: J Inherit Metab Dis. 2012 Jan 10;36(2):221–225. doi: 10.1007/s10545-011-9438-x

Table 2.

Subtype of MPS, RHI and Echocardiographic Findings in MPS Patients

Subject MPS Type-Rx RHI Shortening Fraction Mitral regurgitation Peak mitral gradient mmHg Aortic regurgitation Peak aortic gradient mmHg
1 I-HSCT 1.00 45 1–2+ * None 13
2 I-HSCT 1.42 40 Trace Normal None Normal
3 II-ERT 1.03 37 Prolapse 1+ Normal Trace mechanical valve 19
4 I-HSCT 1.49 38 * E=9 Trace-1+ 10
5 VI-ERT 1.41 34 Prolapse 1+ Normal Trace Normal
6 II-ERT 1.12 44 1+ 3 None 3
7 II-ERT 1.14 43 None Normal * 19
8 II-ERT 1.09 39 1+ Normal 2–3+ Normal
9 II-ERT 1.01 48 1+ Normal None Normal
10 I-ERT 1.11 49 None None None None
11 VI-HSCT 1.31 * * * * *
12 VI-ERT 1.51 * * * * *

Rx = treatment type;

*

= data unavailable.