Table 4.
Type of congenital heart defect (CHD) and survival among infants with isolated CHD
| Type (RACHS-1 Category)1/ | Total N |
N died ≤ 12 h | N (%) survivors > 12 h 2/ | Total died before initial discharge | N (%) survivors to discharge 2/ | Died after initial discharge | N (%) survivors to 18–22 mo2/ | N (%) 18–22 mo survivors with follow-up |
|---|---|---|---|---|---|---|---|---|
| Tetralogy of Fallot +/− pulmonary atresia (2–3) | 15 | 0 | 15 (100) | 8 | 7 (47) | 2 | 5 (33) | 5/ 5 (100) |
| Transposition of great vessels (3–4) | 5 | 1 | 4 (80) | 2 | 3 (60) | 2 | 1 (20) | 1/ 1 (100) |
| Pulmonary atresia (3–4) | 6 | 0 | 6 (100) | 4 | 2 (33) | 0 | 2 (33) | 2/ 2 (100) |
| Truncus arteriosus (4) | 1 | 0 | 1 (100) | 1 | 0 (0) | - | 0 (0) | - |
| Total anomalous pulmonary venous return (4) | 3 | 0 | 3 (100) | 2 | 1 (33) | 0 | 1 (33) | 0/ 1 (0) |
| Partial anomalous pulmonary venous return (1) | 2 | 0 | 2 (100) | 0 | 2 (100) | 0 | 2 (100) | 2/ 2 (100) |
| Hypoplastic left heart syndrome (6) | 9 | 2 | 7 (78) | 9 | 0 (0) | - | 0 (0) | - |
| Hypoplastic right heart syndrome (3–6) | 2 | 0 | 2 (100) | 2 | 0 (0) | - | 0 (0) | - |
| Coarctation of aorta (2) | 9 | 0 | 9 (100) | 5 | 4 (44) | 0 | 4 (44) | 2/ 4 (50) |
| Complete atrioventricular canal 3/ (3) | 3 | 0 | 3 (100) | 2 | 1 (33) | 0 | 1 (33) | 1/ 1 (100) |
| Single ventricle (3–6) | 1 | 1 | 0 (0) | 1 | 0 (0) | - | 0 (0) | - |
| Double outlet right ventricle (3) | 5 | 0 | 5 (100) | 3 | 2 (40) | 0 | 2 (40) | 2/ 2 (100) |
| Tricuspid atresia (4) | 1 | 0 | 1 (100) | 1 | 0 (0) | - | 0 (0) | - |
| Atrial septal defect (1–2) | 11 | 0 | 11 (100) | 2 | 9 (82) | 0 | 9 (82) | 9/ 9 (100) |
| Ventricular septal defect (2) | 20 | 0 | 20 (100) | 3 | 17 (85) | 0 | 17 (85) | 14/ 17 (82) |
| Pulmonary valve stenosis (2) | 10 | 0 | 10 (100) | 0 | 10 (100) | 1 | 9 (90) | 7/ 9 (78) |
| Other cardiovascular anomalies 4/ | 7 | 1 | 6 (86) | 3 | 4 (57) | 0 | 4 (57) | 4/4 (100) |
| Total | 110 | 5 | 105 (95) | 48 | 62 (56) | 5 | 57 (52) | 49/ 57 (86) |
Risk Adjustment in Congenital Heart Surgery (RACHS)-1 Category [8]
Percents are among total number of infants with each CHD. Number of survivors to 18–22 months includes children lost to follow-up but presumed alive.
Includes 1 infant with complete AV canal and Tetralogy of Fallot.
Includes large aortopulmonary collaterals (n=1), hypoplastic pulmonary arteries (n=1), right coronary artery originating from left cusp (n=1), anomalous left coronary artery (n=1), hypoplastic aortic arch (n=1), univentricular heart with common AV valve, total anomalous venous return and pulmonic stenosis (n=1), and multiple cardiac anomalies [partial anomalous pulmonary venous return to the superior vena cava, left pulmonary stenosis, secundum ASD, anomalous coronary artery (n=1)]