Table I.
Diagnosis, ICD codes, and numbers of PID patients
| Diagnosis | ICD code |
Patient count |
Percent |
|---|---|---|---|
| Hypogammaglobulinemia unspecified |
279.00 | 490 | 17.96 % |
| Unspecified immune deficiency | 279.3 | 477 | 17.48 % |
| Selective deficiency IgG | 279.03 | 274 | 10.04 % |
| DiGeorge syndrome | 279.11 | 249 | 9.12 % |
| Common variable Immunodeficiency | 279.06 | 242 | 8.87 % |
| Selective IgA Immunodeficiency | 279.01 | 215 | 7.88 % |
| Single Complement Deficiency | 279.8 | 205 | 7.51 % |
| Immunodeficiency with predominant T-cell defect |
279.10 | 169 | 6.19 % |
| Unspecified disorder of immune mechanism |
279.9 | 147 | 5.39 % |
| Combined immunodeficiency (includes SCID) |
279.2 | 143 | 5.24 % |
| Selective IgM Immunodeficiency | 279.02 | 34 | 1.25 % |
| Wiskott-Aldrich syndrome | 279.12 | 30 | 1.10 % |
| Congenital hypogammaglobulinemia (Agammaglobulinemia) |
279.04 | 22 | 0.81 % |
| Transient hypogammaglobulinemia | 279.09 | 17 | 0.62 % |
| Hyper-IgM | 279.05 | 10 | 0.37 % |
| Autoimmune disease not elsewhere classified |
279.4 | 3 | 0.11 % |
| Nezelof’s syndrome | 279.13 | 2 | 0.07 % |
| Total | 2729 | 100.00 % |