Table 1.
ID | Age (years) | Gender | Disease | Disease duration | Total ICARS (max. 100) | Stand and Gait (max. 34) | Kinetic Function (max. 52) | Dysarthria (max. 8) | Oculomotor function (max. 6) |
---|---|---|---|---|---|---|---|---|---|
Cerebellar degeneration | |||||||||
cer-deg-1 | 34 | F | SAOA | 7 years | 51 | 25 | 18 | 2 | 6 |
cer-deg-2 | 44 | M | SAOA | 6 years | 12 | 7.5 | 2.5 | 2 | 0 |
cer-deg-3 | 45 | M | SAOA | 15 years | 27.5 | 10 | 12.5 | 4 | 1 |
cer-deg-4 | 46 | F | ADCA III | 28 years | 26.5 | 8 | 11 | 2.5 | 5 |
cer-deg-5 | 48 | F | ADCA III | 8 years | 12.5 | 3 | 5 | 3.5 | 1 |
cer-deg-6 | 49 | M | SAOA | 13 years | 41 | 8 | 26 | 2 | 5 |
cer-deg-7 | 49 | M | ADCA III | 10 years | 44 | 21 | 15 | 4 | 4 |
cer-deg-8 | 49 | M | ADCA III | 9 years | 27.5 | 10.5 | 9 | 2 | 6 |
cer-deg-9 | 52 | F | SCA14 | 13 years | 23 | 9 | 12 | 1 | 1 |
cer-deg-10 | 52 | M | Cerebellitis | 9 years | 50 | 25 | 16 | 4 | 5 |
cer-deg-11 | 54 | M | SAOA | 19 years | 51 | 25 | 17 | 4 | 5 |
cer-deg-12 | 56 | F | SCA 6 | 7 years | 26.5 | 7 | 14.5 | 0 | 5 |
cer-deg-13 | 58 | F | ADCA III | 18 years | 24 | 1 | 21 | 2 | 0 |
cer-deg-14 | 62 | M | SAOA | 13 years | 25.5 | 10.5 | 9 | 1 | 5 |
cer-deg-15 | 62 | M | SAOA | 8 years | 22.5 | 7 | 13.5 | 2 | 0 |
cer-deg-16 | 72 | M | SAOA | 6 years | 24 | 7.5 | 9.5 | 1 | 6 |
cer-deg-17 | 72 | M | SCA6 | 16 years | 63 | 29.5 | 24 | 4.5 | 5 |
cer-deg-18 | 73 | M | SCA6 | 12 years | 40.5 | 15.5 | 15 | 4 | 6 |
cer-deg-19 | 74 | F | SCA6 | 7 years | 39.5 | 15 | 16.5 | 3 | 5 |
Cerebellar stroke | |||||||||
cer-foc-1 | 32 | F | PICA left | 3.1 years | 0 | 0 | 0 | 0 | 0 |
cer-foc-2 | 33 | F | PICA right | 9 days | 4 | 4 | 0 | 0 | 0 |
cer-foc-3 | 36 | M | PICA left | 1.6 years | 0 | 0 | 0 | 0 | 0 |
cer-foc-4 | 41 | M | SCA left, PICA right | 8.6 years | 0 | 0 | 0 | 0 | 0 |
cer-foc-5 | 43 | M | SCA right | 2.3 years | 2 | 1 | 1 | 0 | 0 |
cer-foc-6 | 44 | F | SCA right | 26 days | 1 | 1 | 0 | 0 | 0 |
cer-foc-7 | 47 | F | PICA right | 10.1 years | 0 | 0 | 0 | 0 | 0 |
cer-foc-8 | 48 | M | SCA right | 1.3 years | 0 | 0 | 0 | 0 | 0 |
cer-foc-9 | 49 | M | PICA left | 8 months | 0 | 0 | 0 | 0 | 0 |
cer-foc-10 | 50 | M | PICA right | 8.6 years | 0 | 0 | 0 | 0 | 0 |
cer-foc-11 | 51 | M | PICA left | 6 months | 4 | 1 | 3 | 0 | 0 |
cer-foc-12 | 52 | M | PICA left | 9.4 years | 0 | 0 | 0 | 0 | 0 |
cer-foc-13 | 54 | M | PICA left | 1.9 years | 4 | 4 | 0 | 0 | 0 |
cer-foc-14 | 55 | M | SCA left | 2.9 years | 3.5 | 1.5 | 2 | 0 | 0 |
cer-foc-15 | 55 | M | PICA left | 36 days | 0.5 | 0.5 | 0 | 0 | 0 |
cer-foc-16 | 56 | M | SCA left | 7.2 years | 4 | 1 | 3 | 0 | 0 |
cer-foc-17 | 56 | M | PICA right | 11.9 years | 1 | 1 | 0 | 0 | 0 |
cer-foc-18 | 56 | F | PICA left | 1 year | 2 | 1 | 1 | 0 | 0 |
cer-foc-19 | 57 | M | SCA left | 11.9 years | 0 | 0 | 0 | 0 | 0 |
cer-foc-20 | 60 | M | SCA right | 6 years | 4 | 1.5 | 2.5 | 0 | 0 |
cer-foc-21 | 60 | M | SCA left | 28 days | 2.5 | 2.5 | 0 | 0 | 0 |
cer-foc-22 | 62 | F | PICA right | 56 days | 2.5 | 1 | 1.5 | 0 | 0 |
cer-foc-23 | 76 | M | SCA right | 9.7 years | 2 | 0 | 2 | 0 | 0 |
cer-foc-24 | 49 | M | Haemorrhage right | 180 days | 34 | 15 | 11.5 | 1.5 | 6 |
cer-foc-25 | 75 | M | PICA left | 13 days | 6.5 | 4 | 2.5 | 0 | 0 |
cer-foc-26 | 44 | M | SCA right | 23 days | 13.5 | 5.5 | 7 | 1 | 0 |
cer-foc-27 | 72 | M | SCA right | 9 days | 2 | 1 | 0.5 | 0.5 | 0 |
SCA6 = spinocerebellar ataxia type 6; SCA14 = spinocerebellar ataxia type 14; SAOA = sporadic adult onset ataxia; ADCA III = autosomal dominant ataxia type III (a pure cerebellar disorder with autosomal dominant inheritance and inconclusive genetic testing); SCA = superior cerebellar artery; PICA = posterior inferior cerebellar artery; ICARS = International Cooperative Ataxia Rating Scale (Trouillas et al., 1997); total ICARS (maximum total score) and ICARS subscores (maximum subscore) are shown; kinetic function = upper and lower limb ataxia; M = male; F = female.