Table 2.
Patient demographic and baseline characteristics in 4 patients ≥19 years of age
| MPS type | n | Age (yr) | Age range (yr) | Height z score | Weight z score | BMI z score | BMD (g/cm2) | BMD T-score |
|---|---|---|---|---|---|---|---|---|
| MPS I (H/S*) |
1 |
22.5 |
22.5 |
−6.38 |
−3.31 |
−1.58 |
0.614 |
−3.49 |
| MPS II |
2 |
22.6 (1.6) |
21.5-23.7 |
−9.15 (0.33) |
−2.54 (0.12) |
0.47 (0.1) |
0.64 (0.006) |
−6.6 (0.07) |
| MPS VI |
1 |
22.8 |
22.8 |
−8.88 |
−3.25 |
−0.11 |
0.712 |
−2.82 |
| Total | 4 | 22.6 (0.9) | 21.5-23.7 | −8.39 (1.36) | −2.91 (0.43) | −0.19 (0.97) | 0.65 (0.04) | −4.88 (2.01) |
Values are displayed as mean (standard deviation).
MPS, mucopolysaccharidoses; H/S*, Hurler/Scheie; z score, standard deviation score; BMI, body mass index; BMD, bone mineral density; HAZ, height-for-age z score.