Table 1.

Stages of ADNIV (autosomal dominant neovascular inflammatory vitreoretinopathy) disease and associated clinical findings

Stage	Anterior segment	Posterior segment	Electroretinogram
Stage I	Rare cells	Rare cells	Reduced b-wave
Stage II	Mild cells Mild posterior subcapsular cataract	Moderate cells Optic disc edema Cystoid macular edema Peripheral pigmentation of the retina	Flat b-wave, normal a-wave
Stage III	Moderate cells Anterior subcapsular cataract Moderate posterior subcapsular cataract Iris synechiae	Moderate cells Vitreous traction at posterior pole Epiretinal membrane Tractional retinal detachment Posterior vitreous bands Peripheral fibrosis Peripheral neovascularization Neovascularization of the disc Pigmentary retinopathy Cystoid macular edema	Flat b-wave, reduced a-wave
Stage IV	Iris bombe, seclusio pupil Peripheral anterior synechiae Angle closure glaucoma Neovascular glaucoma	Moderate cells Vitreous hemorrhage Posterior tractional retinal detachment Anterior tractional retinal detachment	Non-recordable electroretinogram
Stage V	Phthisis	Combined tractional and rhegmatogenous retinal detachment Phthisis