Table 2. Description of PXE patients with proved or suspected coronary artery disease.

Patient	Age	Gender	CV Risk Factors	History of coronary artery disease	Results of investigations
1	60	M	BMI  = 36, Familial history of CAD	Angioplasty and stent in the RCA because of exercise angina at 53 year-old	Asymptomatic, Inferior Q wave, Akinetic inferior wall on echography, Negative treadmill-test/year, Scar in 2 inferior segments on MRI
2	49	M	BMI  = 28, Tobacco use	NST-ACS at 46 year-old, Distal occlusion of LAD with collateral circulation, No angioplasty	No Angina, Dyspnea because of severe precapillary pulmonary hypertension
3	39	F	None	CABG at 10 year-old because of angina due to severe LAD stenosis and RCA occlusion.	Asymptomatic, Negative scintigraphy Functional grafts on computed tomography angiography
4	73	F	Dyslipidemia, Familial history of CAD	Chest pain during exercise in 2000, Negative treadmill-test in 2000	Asymptomatic, Negative treadmill-test, Normal ECG and CMR
5	43	F	Hypertension	Chest pain at night only: spastic angina?	Negative treadmill-test and negative scintigraphy
6	40	F	Tobacco use	Atypical chest pain	Normal CMR, Normal ECG, Negative treadmill-test and negative scintigraphy

CV indicates cardiovascular; M, male; F, female; BMI, body mass index (kg/m2); NST-ACS, non ST-acute coronary syndrome; CAD, coronary artery disease, CMR, cardiac magnetic resonance imaging.