TABLE 4.

N370S Homozygote and Compound Heterozygote Comparison Statistics

Variable	N370S Homozygotes(n=19)		N370S Heterozygotes (n= 28)		Pa
	Median	Quantile (25–75%)	Median	Quantile (25–75%)
No. of women	15(79%)		12(43%)		0.02b,c
Age(y)	50	37–55	46	33–51	0.33
Duration of enzyme replacement therapy (y)	6	0–8	7	1–11	0.15
Liver volume (cm3)	1,503	1,072–1,798	1,578	1,193–1,911	0.55
Spleen status score	1	0–1	2	1–2	<0.001c
Bone marrow burden score
Lumbar spine	3	0–4	5	3–7	<0.01c
Femur	3	3–5	6	4–7	<0.01c
Total	6	3–8	10	8–13	<0.001c

^aWilcoxon's test.

^bFisher's exact probability.

^CStatistically significant.