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. Author manuscript; available in PMC: 2013 Aug 5.
Published in final edited form as: Blood Rev. 2010 Apr 24;24(3):101–122. doi: 10.1016/j.blre.2010.03.002

Figure 3.

Figure 3

Age at diagnosis of cases reported in the literature in the major IBMFS. FA, Fanconi Anemia. DC, Dyskeratosis Congenita. DBA, Diamond-Blackfan Anemia. SDS, Shwachman-Diamond Syndrome. FA, age available in 1497/2002 case reports; median age 6.5 years, range 0–49. DC, age available for 467/550 case reports; median age 14 years, range 0–75. DBA, age available for 722/980 case reports; median 3 months, range birth-64 years. SDS, age available for 318/563 case reports; median 2 weeks, range birth-11 years. Note the different X-axes. Insets in DBA and SDS extend to older patients, representing <3% of the total number for each syndrome.