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. 2013 Aug;59(8):837-840.

Figure 1.

Figure 1

Metabolic pathway in individuals unaffected by PKU: Normal function of PAH and BH4 resulting in normal conversion of Phe to Tyr.

BH4 —tetrahydrobiopterin, PAH—phenylalanine hydroxylase, Phe—phenylalanine, PKU—phenylketonuria, Tyr—tyrosine.