Official websites use .gov
A
.gov website belongs to an official
government organization in the United States.
Secure .gov websites use HTTPS
A lock (
) or https:// means you've safely
connected to the .gov website. Share sensitive
information only on official, secure websites.
Metabolic pathway in individuals with PKU: Absence or severe reduction of PAH with normal BH4 resulting in accumulation of Phe and reduction of Tyr.
BH4 —tetrahydrobiopterin, PAH—phenylalanine hydroxylase, Phe—phenylalanine, PKU—phenylketonuria, Tyr—tyrosine.
