Table 2. Clinical features of 12 BrS patients experiencing lifetime MAE.
| ID | Year of birth | Age at MAE | Sex | Family history for SCD | s-Type I ECG | Result EPS | Syncope | SVA | MAE | SCN5A mutation |
|---|---|---|---|---|---|---|---|---|---|---|
| 071603P | 1957 | 50 | M | − | + | nd | + | − | CA | − |
| 09193P | 1974 | 35 | M | − | + | + | − | − | ICD shock | − |
| 062293P | 1976 | 30 | M | − | − | + | − | + | VT/VF | − |
| 0711P | 1954 | 54 | M | + | + | + | + | − | ICD shock | − |
| 061352P | 1981 | 25 | M | − | − | − | + | − | VFL/VF | p.E1225K |
| 05256P | 1958 | 47 | M | − | − | − | − | + | CAa | − |
| 081712P | 1953 | 49 | M | − | − | − | + | + | VT/VF, CA | p.R104Q |
| 063003P | 1980 | 27 | M | − | + | nd | − | − | VF | p.A1428S |
| 092941P | 1969 | 40 | M | − | − | − | + | − | VF | − |
| 073671P | 1974 | 31 | M | − | + | + | + | + | VT/VF | p.L276Q |
| 062107P | 1945 | 61 | M | + | − | + | + | − | VT/VF | − |
| 053609P | 1949 | 56 | M | − | − | + | + | + | VF | − |
Abbreviations: CA, cardiac arrest; EPS, electrophysiological study; M, male; MAE, major arrhythmic event; nd, not done; s-Type I, spontaneous type I ECG, SVA, supraventricular arrhythmias; VF, ventricular fibrillation; VFL, ventricular flutter; VT/VF, polymorphic ventricular tachycardia degenerating in fibrillation.
a
After propafenone administration.