Table 2.
Clinical Characteristics
| Patient | IIIa vs IIIb | Major Cardiac Event | Cardiac Symptoms at Last Clinic Visit |
|---|---|---|---|
| A-1 | A | None | None |
| A-2 | A | None | Tired after activity |
| A-3 | A | Sudden death @ age 36 yrs | Chest pain w/exercise; referred for cardiology evaluation |
| A-4 | A | None | None |
| A-5 | A | None | None |
| A-6 | A | Liver, Kidney, Heart Transplant @ age 40 yrs | Congestive heart failure pretransplant |
| A-7 | A | None | None |
| A-8 | A | None | None |
| A-9 | A | None | None |
| A-10 | A | Sudden death @ age 15 yrs | Intermittent chest pain sometimes after exercise |
| A-11 | A | None | None |
| A-12 | A | None | Pleuritic right sided chest pain |
| A-13 | A | None | None |
| A-14 | A | None | Occasional orthostatic dizziness |
| A-15 | A | None | None |
| A-16 | A | None | None |
| A-17 | A | None | None |
| A-18 | A | None | Squeezing chest pain sometimes during strenuous exertion |
| A-19 | A | None | None |
| A-20 | A | None | Dyspnea on exertion; atypical chest pain; peripheral edema |
| A-21 | A | None | Chest pain on one occasion (associated w/diabetic ketoacidosis) |
| A-22 | A | Sudden death @ age 25 yrs | None |
| A-23 | A | None | None |
| B-1 | B | None | None |
| B-2 | B | None | None |
| B-3 | B | None | None |
| B-4 | B | None | None |
| B-5 | B | None | None |
| B-6 | B | None | None |
| B-7 | B | None | Fatigue; Dyspnea w/ exertion; Chest pain w/ and w/o exercise |
| B-8 | B | None | None |
| B-9 | B | Death @ age18 yrs due to pulmonary hypertension | Not available |
| B-10 | B | None | None |