Table 4.

Electrocardigoram, Cardiac Magnetic Resonance, and Cardiopulmonary Exercise Test

		p
ECG (n=24)
Normal Sinus Rhythm	100% (24)
Bundle Branch Block % (n)
None	36% (9)
RBBB	42% (10)
Bifascicular Block	4% (1)
Intraventricular Conduction Delay	17% (4)
Cardiac Magnetic Resonance (n=23)
Pulmonary regurgitant fraction (%) (n=20)	34% (range: 0-47%)
Indexed LV EDV (ml/sqm) (n=23)	98.4 ± 37.6
Indexed LV SV (ml/sqm) (n=23)	63.0 ± 23.2
LV ejection fraction (n=23)	64.7 ± 8.0
Indexed LV Cardiac Index (L/min/sqm) (n=22)	4.1 ± 1.0
Indexed LV Mass (g/sqm) (n=22)	53.5 ± 19.3
Indexed RV EDV (ml/sqm) (n=23)	92.9 ± 32.9
Indexed RV SV (ml/sqm) (n=22)	71.3 ± 19.2
RV ejection fraction (n=23)	61.6 ± 7.7
Indexed RV Cardiac Index (L/min/sqm) (n=22)	4.1 ± 1.0
Indexed RV Mass (n=22)	71.3 ± 19.2
Cardiopulmonary Exercise Test (n=22)
Maximal Effort % (n)* (n=20)	50% (10)
Respiratory exchange ratio (n=20)	1.12 (1.09-1.34)
Maximum heart rate (n=19)	179 ± 10
Forced Vital Capacity (L) (n=19)	2.2 ± 0.8
Predicted Forced Vital Capacity (%)(n=19)	75.6 ± 16.8	<0.0001
FEV1/FVC (n=19)	0.87 ± 0.08
Maximum Oxygen Consumption (mVO2) (ml/kg/min) (n=20)	29.3 ± 8.9
Percent predicted mVO2 (n=20)	75.3 ± 24.3	<0.0002
VAT (ml/kg/min) (n=20)	19.2 ± 5.1
Percent predicted VAT (n=20)	86 ± 22	0.01
Maximum work (watts/kg) (n=17)	2.3 ± 0.7	<0.0001
Percent predicted max work (n=17)	74 ± 19
Indexed O2 pulse (mlO2/beat/sqm) (n=20)	4.9 ± 1.3

Abbvreviations: EDV: end-diastolic volume, FEV1/FVC: one-second forced expiratory volume / forced vital capacity, LV: left ventricle, RBBB: right bundle branch block, RV: right ventricle, SV: stroke volume, VAT: oxygen consumption at anaerobic threshold

Data are expressed as mean (± SD), median (range), or percentage (number).

^*Maximal effort is defined as RQ ≥ 1.1 at peak exertion