. Author manuscript; available in PMC: 2014 Sep 1.

Published in final edited form as: Mol Genet Metab. 2013 Jun 26;110(0):129–138. doi: 10.1016/j.ymgme.2013.06.008

Table 3.

KS and GAG levels in MPS IVA patients and control subjects

	Control	Blood KS (ng/ml)	Urine KS (mg/gCr)	Urine GAGs (mg/gCr)	MPS IVA	Blood KS (ng/ml)	Urine KS (mg/gCr)	Urine GAGs (mg/g Cr)
Under 0.5 years^#	Mean	46.5	0.22	287	Mean
	SD	24.9	0.18	125	SD
	n	51	44	44	n

0.5 years to 5 years^*	Mean	149	0.24	144	Mean	567	5.5	217
	SD	60	0.14	88	SD	240	9.0	85.1
	n	45	53	54	n	13	11	11

5 to 15 years^**	Mean	203.5	0.24	53.6	Mean	548	3.6	161
	SD	82.7	0.14	42.6	SD	286	4.7	100
	n	32	44	29	n	19	18	21

Over 15 years^***	Mean	145.1	0.12	44.2	Mean	323	1.07	81.6
	SD	59.4	0.07	32.9	SD	207	0.53	28.7
	n	106	37	38	n	6	4	4

Data is not available in MPS IVA patient

Blood KS, P < 0.0001; urine KS, P = 0.082; urine GAGs, P = 0.021

^**

Blood KS, P < 0.0001; urine KS, P = 0.008; urine GAGs, P < 0.0001

^***

Blood KS, P = 0.089; urine KS, P = 0.037; urine GAGs, P = 0.073