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. 2013 Jun 16;22(21):4349–4356. doi: 10.1093/hmg/ddt284

Table 2.

Demographics and patient characteristics

NP-C positive (n = 3) NP-C uncertain (n = 12) NP-C negative (n = 235)
Gender (male:female) 1:2 8:4 161:74
Age in years, median (range) 43 (41–49) 36 (22–57) 38 (18–90)
Primary diagnosis, n
 Psychosis 0 9 153
 Early-onset progressive cognitive decline 2 1 48
 Psychosis combined with early-onset progressive cognitive decline 1 2 34
Neurological symptoms, n
 Presenta 3 9 210
  Focal dystonia 0 3 71
  Cerebellar ataxia 2 3 66
  Dysarthria 3 7 133
  VSGPb 2 1 38
  Epilepsy 0 2 65
  Cataplexy 1 1 5
 Absent 0 3 21
 Unknown 0 0 4
Visceral symptoms, n
 Presenta 1 1 32
  Hepatomegaly 0 1 30
  Splenomegaly 1 0 7
 Absent 1 9 158
 Unknown 1 2 45

aMultiple answers possible.

bVertical supranuclear gaze palsy (positive clinical assessment at baseline visit).