Table 5.
Type A | Type B | Type C | Type D | |
Symptoms | Absent or mild | Moderate or severe | Severe (or moderate) | Severe (or moderate) |
Cyst characteristics | Any | Limited No. large cysts | Any | Any |
Areas of relative normal liver parenchyma | Any | ≥ 2 sectors | ≥ 1 sector | < 1 sector |
Presence of portal vein or hepatic vein occlusion in the preserved hepatic sectors | Any | Absent | Absent | Present |
Recommended therapy | Observation or medical therapy | Cyst fenestration | Partial hepatectomy with possible fenestration of remnant cysts | Liver Transplantation |