Table 2.
Initial workup | VWF:Ag, VWF:RCo, FVIII:C, multimers1 |
If ↓ VWF:RCo/VWF:Ag, abnormal multimers | LD-RIPA, VWF:PB, consider sequencing |
If ↓ VWF:RCo/VWF:Ag, normal multimers | Consider sequencing |
If ↓ FVIII:C/VWF:Ag | VWF:FVIIIB |
If ↓↓ VWF:RCo and VWF:Ag | VWFpp, survival studies |
Abbreviations: VWF:Ag=VWF antigen; VWF:RCo=VWF ristocetin cofactor activity; FVIII:C=factor VIII activity; multimers=multimer distribution analysis; LD-RIPA=low dose ristocetin-induced platelet aggregation; VWF:PB=VWF-platelet binding; VWF:FVIIIB=VWF-FVIII binding; VWFpp=VWF propeptide.
Repeat VWF:Ag and VWF:RCo to confirm low levels