Table 3.
VWD diagnosis | Laboratory findings |
Type 1 | ↓ (but proportional) VWF:Ag and VWF:RCo with normal multimers |
Type 1C | ↓ VWF:Ag with ↑ VWFpp/VWF:Ag ratio |
Type 2A | ↓ VWF:RCo/VWF:Ag ratio with abnormal multimers |
Type 2B | ↓ VWF:RCo/VWF:Ag ratio with abnormal multimers and ↑ LD-RIPA, abnormal VWF:PB, possible thrombocytopenia |
Type 2M | ↓ VWF:RCo/VWF:Ag ratio with normal multimers |
Type 2N | ↓ FVIII:C/VWF:Ag and abnormal VWF:FVIIIB |
Type 3 | Absent VWF:Ag and VWF:RCo |
Abbreviations: VWF:Ag=VWF antigen; VWF:RCo=VWF ristocetin cofactor activity; FVIII:C=factor VIII activity; multimers=multimer distribution analysis; LD-RIPA=low dose ristocetin-induced platelet aggregation; VWF:PB=VWF-platelet binding; VWF:FVIIIB=VWF-FVIII binding; VWFpp=VWF propeptide.