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. Author manuscript; available in PMC: 2014 Nov 1.
Published in final edited form as: Am J Hematol. 2013 Aug 1;88(11):10.1002/ajh.23532. doi: 10.1002/ajh.23532

Table 1. Patient Demographics.

Clinical Features of 23 patients with Sickle Cell Disease and acute VOC

Feature Number (%)

Males: 7 (30%)

Mean Age (standard deviation) 34.3 (7.96)

Number of patients with SS/SC/ST 22/1/0

Deaths 1 (4%)

Race
 African American 10 (44%)
 African 7 (30%)
 Hispanic/Latino 6 (26%)

Number of Patients with Liver Biopsy 15 (65%)
 Ishak Fibrosis Score 0–2 14 (93%)
 Ishak Fibrosis Score 3–4 1 (7%)
 Ishak Fibrosis Score 5–6 0 (0%)

Liver Biopsy Features Median (Range)

HAI Total Inflammation (0–18) 3.0 (0–8)

Ishak Fibrosis (0–6) 0 (0–3)

Iron Score (0–4) 3.0 (1–4)

Liver Iron Concentration (normal: 200–2400 mcg/g dry weight) 6943 (1907–36416)

Deugnier Score 28 (10–46)

Abbreviations: VOC, vaso-occlusive crisis; HAI, Histologic Activity Index