TABLE 2.
DEMOGRAPHIC AND KEY CLINICAL CHARACTERISTICS OF THE 6 PATIENTS WITH CRANIOFACIAL DYSOSTOSIS (APERT SYNDROME) WHOSE INFERIOR OBLIQUE MUSCLE SPECIMENS WERE STUDIED
SUBJECT | GENDER |
AGE AT SURGERY (YEARS) |
VISUAL ACUITY (OD, OS) |
IO OVERACTION & UNDERACTION* |
SPECIMEN COLLECTED (OD OR OS) |
PREVIOUS IO SURGERY |
---|---|---|---|---|---|---|
1 | F | 4 | GCM, GCM | N/A | OD and OS | Anterior nasal transposition |
2 | M | 8 | HM, 20/50 | +3RIO, +4LIO | OD and OS | Nasal myectomy (bilateral) |
3 | F | 2 | GCUM, GCM | +3 RIO, +3 LIO | OD and OS | NPS |
4 | F | 3 | GCM, GCM | +3RIO, +3LIO | OD | NPS |
5 | F | 5 | 20/40, 20/50 | +3LIO | OD | NPS |
6 | F | 7 | 20/25, 20/25 | +2RIO | OS | NPS |
F, female; GCM, good, central, maintained; GCUM, good, central, unmaintained; IO, inferior oblique muscle; LIO, left inferior oblique muscle; M, male; NPS, no prior surgery; OD, right eye; OS, left eye; RIO, right inferior oblique muscle.
According to the Elliott and Parks grading scale.58