Table 4.

Previous and Current Nomenclature

Previous nomenclature	Current nomenclature
von Willebrand’s disease	von Willebrand disease
vWF	VWF
vWD	VWD
RiCof (ristocetin cofactor activity)	VWF:RCoa
FVIII RAg (FVIII related antigen)	VWF:Aga
Platelet-type VWD	Platelet-type pseudo-von Willebrand disease (PT- VWD), caused by mutations in GPIBA and thus not a form of VWD
Acquired VWD	Acquired von Willebrand syndrome (AVWS)17 is the preferred terminology for defects in VWF concentration, structure or function that are neither inherited nor reflective of mutations in the VWF gene, but which arise as consequences of other medical conditions

^aRecommended abbreviations for VWF and its activities are detailed in Mazurier and Rodegheiro¹¹⁰