Skip to main content
. Author manuscript; available in PMC: 2013 Dec 2.
Published in final edited form as: J Pediatr Surg. 2012 Nov;47(11):10.1016/j.jpedsurg.2012.07.003. doi: 10.1016/j.jpedsurg.2012.07.003

Table 1.

Clinical Characteristics and Outcomes

Case No Age* Gender Mutation Largest lesion size (cm) PA Operationsa Recurrence site/time Path Follow up (yrs) Steroids
1 17 M 167: Arg>Gln 3.0 lap-RPA None Pheo 15.63 No
2 13 M 167: Arg>Gln 2.7 lap-LPA, lap-BPA None Pheo 15.77 No
3 13 M 128: Leu>Phe 2.5 open-LPA None Pheo 12.74 No
4 13 M 167: Leu>Gln 4.1 lap-LPA, lap-RPA None Composite 9.41 No
5 15 F 161: Leu>Gln 1.4 lap-LPA, lap-RPA None Pheo 2.56 No
6 6 M 124: Thr>Ile 3.5 lap-LPA, lap-RPA Right/5mos Composite 4.58 No
7 17 F 149: Ala>Ser 2.0 open-BPA None Pheo ** **
8 13 M 167: Leu>Gln 1.5 lap-RPA None Pheo 5.00 No
9 16 M 167: Arg>Gln 6.5 open-RPA, lap-RPA Right/1yr Pheo 4.06 No
10 15 M 129: Leu>Pro 5.5 robo-LPA, robo-RPA None Pheo 4.42 Yes x2 years post-op
*

Age at first operation

**

Post-operative death

a

Operations are in chronological order and do not include total adrenalectomies.

Patient was steroid independent for 10 years post operatively. He has recently begun steroid supplementation after removal of an ACTH secreting ectopic tumor in the lung.

lap - laparoscopic

robo - robotic

LPA – left partial adrenalectomy

RPA – right partial adrenalectomy

BPA – bilateral partial adrenalectomy