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. 2013 Aug 22;11(1):11. doi: 10.1186/1897-4287-11-11

Table 1.

Cancer incidence and types of tumors in VHL disease[6]

Type of cancer Cancer incidence
CNS
 
  Hemangioblastomas of the retina
25-60%
  Endolymphatic Sac Tumors
10%
  Hemangioblastomas of
 
  Cerebellum
44-72%
  Brain stem
10-25%
  Spinal cord
13-50%
  Nerve roots L/S
< 1%
  Supratentorial region
< 1%
Organs
 
  Renal cel carcinoma
25-60%
  Pheochromocytoma
10-20%
  Pancreatic tumors
35-70%
  Epididymal cystadenomas 25-60%