Table 2.
Clinical findings in Asian patients: classic versus atypical.
| Classic | Atypical | P value* | |
|---|---|---|---|
| N = 9 | N = 12 | ||
| Age at onset (years) | 6.7 (2–10) | 30.7 (17–51) | <0.05 |
| Dysarthria | 89% | 42% | |
| Gait disturbance | 89% | 50% | |
| Dystonia | 78% | 75% | |
| General dystonia | 67% | 0% | <0.05 |
| Cranial dystonia | 22% | 50% | |
| Segmental dystonia | 0% | 67% | <0.05 |
| Dysphagia | 56% | 8% | <0.05 |
| Pyramidal signs | 56% | 17% | |
| Mental impairment | 44% | 8% | |
| Limb chorea | 44% | 8% | |
| Tremors | 22% | 83% | <0.05 |
| Parkinsonism | 11% | 42% | |
| Psychiatric symptoms | 0% | 0% |
*Blank indicates it does not reach statistical significance (P ≥ 0.05).