CHART 1.

Information about PPV classifications

Type	Type	Vascular lesion	Pigmentary lesion
(according to Happle)	(according to Hasegawa*)
(inexistent**)	I	Nevus flammeus	Verrucous and pigmented nevus
Cesioflammea	II	Nevus flammeus ± anemic nevus	Mongolian spot
Spilorosea	III	Nevus flammeus ± anemic nevus	Nevus Spilus
Non-classifiable	IV	Nevus flammeus ± anemic nevus	Mongolian spot, Nevus Spilus
Cesiomarmorata	V	Cutis Marmorata Telangiectatica Congenita	Mongolian spot

* All subtypes, according to Hasegawa, are subdivided in types (a) or (b) - with and without systemic involvement, respectively

** According to Happle, the subtype I does not exist for there are no reported cases to this day

Source: Happle R. 2005⁶ e Hasegawa Y, et al. 1985.³