Table 1.
Multicenter study* | This study | |
---|---|---|
Anti-Mi-2 (+) pts., number (%) | 9/376 (2.4) | 7/124 (5.6) |
Age at onset, median (range), y | 45 (16–66) | 62 (40–73) |
Sex, M/F, number | 6/3 | 1/6 |
Diagnosis, % | ||
Classical DM | 100 | 100 |
Clinically amyopathic DM | 0 | 0 |
Clinical features, % | ||
Muscle weakness | 100 | 100 |
Arthritis | 11 | 14 |
ILD | 11 | 0 |
Malignancy | 0 | 0 |
Skin eruptions, % | ||
Heliotrope rash | 67 | 57 |
Facial erythema** | 56 | 100 |
Gottron sign | 89 | 100 |
Prognosis (alive), % | 100 | 100 |
*Data from [10]. This cohort includes 7 patients used in this study, all of whom were negative for anti-Mi-2 antibodies. **Facial erythema other than heliotrope rash.