. Author manuscript; available in PMC: 2014 Jun 19.
Published in final edited form as: J Cyst Fibros. 2012 Dec 20;12(2):116–124. doi: 10.1016/j.jcf.2012.11.010
© 2012 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.