Skip to main content
. 2013 Jan 1;2(1):6–19. doi: 10.5812/nephropathol.8971

Table 1. The Chapel Hill Consensus Conference classification of vasculitis (4).

Large blood vessels vasculitis
Takayasu arteritis
Temporal arteritis
Medium-sized blood vessels vasculitis
Polyarteritis nodosa
Kawasaki disease
Central nervous system isolated angiitis
Small blood vessels vasculitis
ANCA-associated small-vessel vasculitis: Microscopic polyangiitis, Wegener’s granulomatosis, Churg–Strauss syndrome, Drug-induced ANCA-associated vasculitis
Immune-complex small-vessel vasculitis
Henoch–Schönlein purpura
Cryoglobulinemic vasculitis
Lupus vasculitis
Rheumatoid vasculitis
Sjögren’s syndrome vasculitis
Hypocomplementemic urticarial vasculitis
Behçet’s disease
Goodpasture’s syndrome
Serum-sickness vasculitis
Drug-induced immune-complex vasculitis
Infection-induced immune-complex vasculitis
Paraneoplastic small-vessel vasculitis
Lymphoproliferative neoplasm-induced vasculitis
Myeloproliferative neoplasm-induced vasculitis
Carcinoma-induced vasculitis
Inflammatory bowel disease vasculitis