Table 1. The Chapel Hill Consensus Conference classification of vasculitis (4).
Large blood vessels vasculitis Takayasu arteritis Temporal arteritis |
Medium-sized blood vessels vasculitis Polyarteritis nodosa Kawasaki disease Central nervous system isolated angiitis |
Small blood vessels vasculitis ANCA-associated small-vessel vasculitis: Microscopic polyangiitis, Wegener’s granulomatosis, Churg–Strauss syndrome, Drug-induced ANCA-associated vasculitis Immune-complex small-vessel vasculitis Henoch–Schönlein purpura Cryoglobulinemic vasculitis Lupus vasculitis Rheumatoid vasculitis Sjögren’s syndrome vasculitis Hypocomplementemic urticarial vasculitis Behçet’s disease Goodpasture’s syndrome Serum-sickness vasculitis Drug-induced immune-complex vasculitis Infection-induced immune-complex vasculitis Paraneoplastic small-vessel vasculitis Lymphoproliferative neoplasm-induced vasculitis Myeloproliferative neoplasm-induced vasculitis Carcinoma-induced vasculitis Inflammatory bowel disease vasculitis |