Table 2. The prevalence of antineutrophil cytoplasmatic autoantibodies (ANCA) in small blood vessels vasculitis (5).
VASCULITIS |
PR3-ANCAa
(C-ANCA , % ) |
MPO-ANCAb
(P-ANCA, %) |
NEGATIVE
ANCA |
Wegener’s granulomatosis | 75 | 20 | 5 |
Microscopic polyangiitis | 40 | 50 | 10 |
Churg-Strauss syndrome | 10 | 60 | 30 |
Microscopic polyangiitis limited to kidney | 20 | 70 | 10 |
a PR3 = proteinase 3; b MPO=myeloperoxidase