Table 2.
Immittance findings for 49 patients with NPC1
| Tympanometry Findings (n=98 ears)
| ||||
|---|---|---|---|---|
| WNL | Abnormal | CNT | ||
|
|
||||
| High | Low | |||
| Vec (cm3) | 79% (77) | 17% (17)* | 4% (4) | |
| Admittance (mmhos) | 80% (78) | 10% (10) | 10% (10) | |
| Negative | Positive | |||
| TPP (daPa) | 50% (49) | 18% (18) | 25% (24) | 7% (7)* |
| Acoustic Reflex Findings (n=22 patients)
| |||
|---|---|---|---|
| WNL | Abnormal | CNT | |
| Acoustic Reflex Thresholds | 9% (2) | 91% (20)** | |
| Acoustic Reflex Adaptation | 27% (6) | 14% (3) | 59% (13) |
Note. WNL, within normal limits; CNT, could not test; Vec, equivalent ear canal volume; TPP, tympanometric peak pressure.
*
Includes four ears with intact, patent pressure equalization tubes
**
60% (12/20) cannot be explained by middle ear status or peripheral hearing thresholds.